Angiomatosis

Medical condition

Angiomatosis

Skin angiomatosis
Specialty	Cardiology

Angiomatosis is a non-neoplastic condition^[1] characterised by nests of proliferating capillaries arranged in a lobular pattern, displacing adjacent muscle and fat.^[2] It consists of many angiomas.^[3]

Presentation

Associated

They often appear in:

Von Hippel–Lindau disease: It can be associated with Von Hippel–Lindau disease and is a rare genetic multi-system disorder characterized by the abnormal growth of tumours in the body. Symptoms may include headaches, problems with balance and walking, dizziness, weakness of the limbs, vision problems and high blood pressure.^[4]
Bacillary angiomatosis
Klippel–Trénaunay syndrome
Sturge–Weber syndrome

Histology

It is a vascular malformation wherein blood vessels proliferate along with accompanying mature fat and fibrous tissue, lymphatics and sometimes nerves.^[2] They may involve skin, subcutaneous tissue, skeletal muscle and occasionally bone.^[2]

Prognosis

Prognosis depends on the size and location of the tumour, untreated angiomatosis may lead to blindness and/ or permanent brain damage. Death may occur, with complications in the kidney or brain.^[4]

References

^ Angiomatosis at the U.S. National Library of Medicine Medical Subject Headings (MeSH)
^ ^a ^b ^c Howat, AJ; Campbell, PE (October 1987). "Angiomatosis: a vascular malformation of infancy and childhood. Report of 17 cases". Pathology. 19 (4): 377–82. doi:10.3109/00313028709103887. PMID 3444663. S2CID 23743347.
^ "angiomatosis" at Dorland's Medical Dictionary
^ ^a ^b "Von Hippel–Lindau Disease (VHL) Information Page". www.ninds.nih.gov. National Institute of Neurological Disorders and Stroke.

External links

Classification	D MeSH: D000798 SNOMED CT: 205562004
External resources	eMedicine: article/1051846

Cardiovascular disease (vessels)

Arteries, arterioles
and capillaries

Inflammation

Peripheral artery disease

Arteriosclerosis	Atherosclerosis Foam cell Fatty streak Atheroma Intermittent claudication Critical limb ischemia Monckeberg's arteriosclerosis Arteriolosclerosis Hyaline Hyperplastic Cholesterol LDL Oxycholesterol Trans fat
Stenosis	Carotid artery stenosis Renal artery stenosis
Other	Aortoiliac occlusive disease Degos disease Erythromelalgia Fibromuscular dysplasia Raynaud's phenomenon

Aneurysm / dissection /
pseudoaneurysm

Vascular malformation

Vascular nevus

Veins

Inflammation	Phlebitis
Venous thrombosis / Thrombophlebitis	primarily lower limb Deep vein thrombosis abdomen Hepatic veno-occlusive disease Budd–Chiari syndrome May–Thurner syndrome Portal vein thrombosis Renal vein thrombosis upper limb / torso Mondor's disease Paget–Schroetter disease head Cerebral venous sinus thrombosis Post-thrombotic syndrome
Varicose veins	Gastric varices Portacaval anastomosis Caput medusae Esophageal varices Hemorrhoid Varicocele
Other	Chronic venous insufficiency Chronic cerebrospinal venous insufficiency Superior vena cava syndrome Inferior vena cava syndrome Venous ulcer

Arteries or veins

Blood pressure

Hypertension	Hypertensive heart disease Hypertensive emergency Hypertensive nephropathy Essential hypertension Secondary hypertension Renovascular hypertension Benign hypertension Pulmonary hypertension Systolic hypertension White coat hypertension
Hypotension	Orthostatic hypotension

v t e Phakomatosis
Angiomatosis	Sturge–Weber syndrome Von Hippel–Lindau disease
Hamartoma	Tuberous sclerosis Hypothalamic hamartoma (Pallister–Hall syndrome) Megalencephaly Multiple hamartoma syndrome Proteus syndrome Cowden syndrome Bannayan–Riley–Ruvalcaba syndrome Lhermitte–Duclos disease
Neurofibromatosis	Type I Type II
Other	Abdallat–Davis–Farrage syndrome Ataxia telangiectasia Incontinentia pigmenti Peutz–Jeghers syndrome Encephalocraniocutaneous lipomatosis